Diagnostics and treatment optimisation of primary immunodeficiency - hereditary angioedema in adults
Karaulov A.V., Sidorenko I.V., Kapustina A.S.
The features of rare form of primary immunodeficiency caused by Ñ1-inhibitor deficiency - hereditary angioedema own data are generalized. Clinical manifestations, immunological features and treatment concepts of hereditary angioedema are marked. The authors suggest the algorithm of early diagnostics and treatment of this primary immunodeficiency in adults, worked out personal self-management plans for every patient and estimated their efficiency.